| Abstract |
H Ranu and SH Pang
Langerhans cell histiocytosis (LCH) is a proliferative histiocytic disorder of unknown cause characterized by the accumulation of Langerhan cells in various tissues. Typically a disorder of childhood, features of this disease have been well documented in children but remain ambiguous and poorly documented in adults leading to many pitfalls in diagnosis. We report a case of Langerhans cell histiocytosis in a young lady who presented with cutaneous involvement of varying morphology and review the various cutaneous manifestations of adult Langerhans cell histiocytosis reported in the literature to date.
郎格罕細胞性組織細胞增生症是一種不明成因的增生性組織細胞疾病，其特徵為郎格罕細胞積聚於多個不同組織。郎格罕細胞性組織細胞增生症為典形的兒童疾病，故兒童的病症特色有著詳盡的記載；但成年患者的記載却相對貧乏及含糊不清，衍生了不少診斷上的困難陷阱。我們報告了一個少女案例，有著多種形態的皮膚影響；繼而就現有文獻中對成年郎格罕細胞性組織細胞增生症患者所報告的種種皮膚表徵進行回顧。
Keywords : Langerhans cell histiocytosis, presentation, treatment
關鍵詞：郎格罕細胞性組織細胞增生症，表現，治療